2022 CDC Clinical Practice Guideline for Prescribing Opioids Implementation Guide
2022.1.0 - CI Build

2022 CDC Clinical Practice Guideline for Prescribing Opioids Implementation Guide, published by Centers for Disease Control and Prevention (CDC). This guide is not an authorized publication; it is the continuous build for version 2022.1.0 built by the FHIR (HL7® FHIR® Standard) CI Build. This version is based on the current content of https://github.com/cqframework/opioid-cds-r4/ and changes regularly. See the Directory of published versions

ValueSet: Sickle-cell diseases

Official URL: http://fhir.org/guides/cdc/opioid-cds/ValueSet/sickle-cell-diseases Version: 2022.1.0
Active as of 2023-05-25 Computable Name: SICKLE_CELL_DISEASES

Copyright/Legal: © CDC 2016+.

Sickle-cell disorders that cause painful crisis

Conditions due to Sickle-cell that can cause painful crisis to be used as exclusions for opioid use recommendations

References

This value set is not used here; it may be used elsewhere (e.g. specifications and/or implementations that use this content)

Logical Definition (CLD)

This value set includes codes based on the following rules:

This value set excludes codes based on the following rules:

 

Expansion

Expansion based on:

  • codesystem International Classification of Diseases, 10th Revision, Clinical Modification (ICD-10-CM) version2024
  • SNOMED CT United States edition 01-Sep 2024

This value set expansion contains 81 concepts.

CodeSystemDisplay
  417357006http://snomed.info/sctSickling disorder due to hemoglobin S (disorder)
  23269001http://snomed.info/sctDouble heterozygous sickling disorder
  25472008http://snomed.info/sctSickle cell-hemoglobin D disease
  35434009http://snomed.info/sctSickle cell-hemoglobin C disease
  36472007http://snomed.info/sctHemoglobin S-F disease
  47024008http://snomed.info/sctSickle cell-hemoglobin E disease
  127040003http://snomed.info/sctSickle cell anemia
  127041004http://snomed.info/sctSickle cell-beta-thalassemia
  127042006http://snomed.info/sctSickle cell beta plus thalassaemia
  127043001http://snomed.info/sctSickle cell-beta^0^-thalassemia
  127044007http://snomed.info/sctSickle cell-delta beta^0^-thalassemia
  127045008http://snomed.info/sctSickle cell anemia with coexistent alpha-thalassemia
  127047000http://snomed.info/sctSickle cell-hemoglobin Lepore disease
  127048005http://snomed.info/sctSickle cell-Hemoglobin O Arab disease
  234391009http://snomed.info/sctSickle cell anemia with high hemoglobin F
  416484003http://snomed.info/sctSickle cell-hemoglobin E disease with crisis (disorder)
  416826005http://snomed.info/sctSickle cell-thalassemia disease with crisis (disorder)
  417048006http://snomed.info/sctSickle cell-thalassemia disease without crisis (disorder)
  417279003http://snomed.info/sctHemoglobin S sickling disorder with crisis (disorder)
  417425009http://snomed.info/sctHemoglobin SS disease with crisis (disorder)
  417517009http://snomed.info/sctSickle cell-hemoglobin C disease with crisis (disorder)
  417748003http://snomed.info/sctSickle cell-hemoglobin D disease with crisis (disorder)
  440206000http://snomed.info/sctHemoglobin SS disease with vasoocclusive crisis (disorder)
  444108000http://snomed.info/sctAcute sickle cell splenic sequestration crisis (disorder)
  783254003http://snomed.info/sctHereditary persistence of fetal hemoglobin with sickle cell disease syndrome
  1153413001http://snomed.info/sctAcute sequestration of spleen due to sickle cell thalassemia with crisis (disorder)
  1153415008http://snomed.info/sctAcute splenic sequestration due to sickle cell hemoglobin C disease with crisis
  10759351000119103http://snomed.info/sctSickle cell anaemia in mother complicating childbirth
  441482006http://snomed.info/sctHistory of sickle cell anaemia
  D57http://hl7.org/fhir/sid/icd-10-cmSickle-cell disorders
  D57.0http://hl7.org/fhir/sid/icd-10-cmHb-SS disease with crisis
  D57.00http://hl7.org/fhir/sid/icd-10-cmHb-SS disease with crisis, unspecified
  D57.01http://hl7.org/fhir/sid/icd-10-cmHb-SS disease with acute chest syndrome
  D57.02http://hl7.org/fhir/sid/icd-10-cmHb-SS disease with splenic sequestration
  D57.03http://hl7.org/fhir/sid/icd-10-cmHb-SS disease with cerebral vascular involvement
  D57.04http://hl7.org/fhir/sid/icd-10-cmHb-SS disease with dactylitis
  D57.09http://hl7.org/fhir/sid/icd-10-cmHb-SS disease with crisis with other specified complication
  D57.2http://hl7.org/fhir/sid/icd-10-cmSickle-cell/Hb-C disease
  D57.20http://hl7.org/fhir/sid/icd-10-cmSickle-cell/Hb-C disease without crisis
  D57.21http://hl7.org/fhir/sid/icd-10-cmSickle-cell/Hb-C disease with crisis
  D57.211http://hl7.org/fhir/sid/icd-10-cmSickle-cell/Hb-C disease with acute chest syndrome
  D57.212http://hl7.org/fhir/sid/icd-10-cmSickle-cell/Hb-C disease with splenic sequestration
  D57.213http://hl7.org/fhir/sid/icd-10-cmSickle-cell/Hb-C disease with cerebral vascular involvement
  D57.214http://hl7.org/fhir/sid/icd-10-cmSickle-cell/Hb-C disease with dactylitis
  D57.218http://hl7.org/fhir/sid/icd-10-cmSickle-cell/Hb-C disease with crisis with other specified complication
  D57.219http://hl7.org/fhir/sid/icd-10-cmSickle-cell/Hb-C disease with crisis, unspecified
  D57.3http://hl7.org/fhir/sid/icd-10-cmSickle-cell trait
  D57.4http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia
  D57.40http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia without crisis
  D57.41http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia, unspecified, with crisis
  D57.411http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia, unspecified, with acute chest syndrome
  D57.412http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia, unspecified, with splenic sequestration
  D57.413http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia, unspecified, with cerebral vascular involvement
  D57.414http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia, unspecified, with dactylitis
  D57.418http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia, unspecified, with crisis with other specified complication
  D57.419http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia, unspecified, with crisis
  D57.42http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta zero without crisis
  D57.43http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta zero with crisis
  D57.431http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta zero with acute chest syndrome
  D57.432http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta zero with splenic sequestration
  D57.433http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta zero with cerebral vascular involvement
  D57.434http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta zero with dactylitis
  D57.438http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta zero with crisis with other specified complication
  D57.439http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta zero with crisis, unspecified
  D57.44http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta plus without crisis
  D57.45http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta plus with crisis
  D57.451http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta plus with acute chest syndrome
  D57.452http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta plus with splenic sequestration
  D57.453http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta plus with cerebral vascular involvement
  D57.454http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta plus with dactylitis
  D57.458http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta plus with crisis with other specified complication
  D57.459http://hl7.org/fhir/sid/icd-10-cmSickle-cell thalassemia beta plus with crisis, unspecified
  D57.8http://hl7.org/fhir/sid/icd-10-cmOther sickle-cell disorders
  D57.80http://hl7.org/fhir/sid/icd-10-cmOther sickle-cell disorders without crisis
  D57.81http://hl7.org/fhir/sid/icd-10-cmOther sickle-cell disorders with crisis
  D57.811http://hl7.org/fhir/sid/icd-10-cmOther sickle-cell disorders with acute chest syndrome
  D57.812http://hl7.org/fhir/sid/icd-10-cmOther sickle-cell disorders with splenic sequestration
  D57.813http://hl7.org/fhir/sid/icd-10-cmOther sickle-cell disorders with cerebral vascular involvement
  D57.814http://hl7.org/fhir/sid/icd-10-cmOther sickle-cell disorders with dactylitis
  D57.818http://hl7.org/fhir/sid/icd-10-cmOther sickle-cell disorders with crisis with other specified complication
  D57.819http://hl7.org/fhir/sid/icd-10-cmOther sickle-cell disorders with crisis, unspecified

Explanation of the columns that may appear on this page:

Level A few code lists that FHIR defines are hierarchical - each code is assigned a level. In this scheme, some codes are under other codes, and imply that the code they are under also applies
System The source of the definition of the code (when the value set draws in codes defined elsewhere)
Code The code (used as the code in the resource instance)
Display The display (used in the display element of a Coding). If there is no display, implementers should not simply display the code, but map the concept into their application
Definition An explanation of the meaning of the concept
Comments Additional notes about how to use the code