2022 CDC Clinical Practice Guideline for Prescribing Opioids Implementation Guide
2022.1.0 - CI Build

2022 CDC Clinical Practice Guideline for Prescribing Opioids Implementation Guide, published by Centers for Disease Control and Prevention (CDC). This guide is not an authorized publication; it is the continuous build for version 2022.1.0 built by the FHIR (HL7® FHIR® Standard) CI Build. This version is based on the current content of https://github.com/cqframework/opioid-cds-r4/ and changes regularly. See the Directory of published versions

ValueSet: Sickle-cell diseases

Official URL: http://fhir.org/guides/cdc/opioid-cds/ValueSet/sickle-cell-diseases Version: 2022.1.0
Active as of 2023-05-25 Computable Name: SICKLE_CELL_DISEASES

Copyright/Legal: © CDC 2016+.

Sickle-cell disorders that cause painful crisis

Conditions due to Sickle-cell that can cause painful crisis to be used as exclusions for opioid use recommendations

References

This value set is not used here; it may be used elsewhere (e.g. specifications and/or implementations that use this content)

Logical Definition (CLD)

This value set includes codes based on the following rules:

  • Include codes fromhttp://snomed.info/sct version 📍 where concept is-a 417357006 (Sickling disorder due to hemoglobin S (disorder))
  • Include codes fromhttp://snomed.info/sct version 📍 where concept is-a 441482006 (History of sickle cell anaemia)
  • Include codes fromhttp://hl7.org/fhir/sid/icd-10-cm version Not Stated (use latest from terminology server) where concept is-a D57 (Sickle-cell disorders)

This value set excludes codes based on the following rules:

  • Exclude codes fromhttp://snomed.info/sct version 📍 where concept is-a 416290001 (Hemoglobin S sickling disorder without crisis (disorder))
  • Exclude codes fromhttp://hl7.org/fhir/sid/icd-10-cm version Not Stated (use latest from terminology server) where concept is-a D57.1 (Sickle-cell disease without crisis)

 

Expansion

Expansion based on:

  • codesystem International Classification of Diseases, 10th Revision, Clinical Modification (ICD-10-CM) version 2024
  • SNOMED CT United States edition 01-Sep 2024

This value set expansion contains 81 concepts.

SystemCodeDisplayJSONXML
http://snomed.info/sct  417357006Sickling disorder due to hemoglobin S (disorder)
http://snomed.info/sct  23269001Double heterozygous sickling disorder
http://snomed.info/sct  25472008Sickle cell-hemoglobin D disease
http://snomed.info/sct  35434009Sickle cell-hemoglobin C disease
http://snomed.info/sct  36472007Hemoglobin S-F disease
http://snomed.info/sct  47024008Sickle cell-hemoglobin E disease
http://snomed.info/sct  127040003Sickle cell anemia
http://snomed.info/sct  127041004Sickle cell-beta-thalassemia
http://snomed.info/sct  127042006Sickle cell beta plus thalassaemia
http://snomed.info/sct  127043001Sickle cell-beta^0^-thalassemia
http://snomed.info/sct  127044007Sickle cell-delta beta^0^-thalassemia
http://snomed.info/sct  127045008Sickle cell anemia with coexistent alpha-thalassemia
http://snomed.info/sct  127047000Sickle cell-hemoglobin Lepore disease
http://snomed.info/sct  127048005Sickle cell-Hemoglobin O Arab disease
http://snomed.info/sct  234391009Sickle cell anemia with high hemoglobin F
http://snomed.info/sct  416484003Sickle cell-hemoglobin E disease with crisis (disorder)
http://snomed.info/sct  416826005Sickle cell-thalassemia disease with crisis (disorder)
http://snomed.info/sct  417048006Sickle cell-thalassemia disease without crisis (disorder)
http://snomed.info/sct  417279003Hemoglobin S sickling disorder with crisis (disorder)
http://snomed.info/sct  417425009Hemoglobin SS disease with crisis (disorder)
http://snomed.info/sct  417517009Sickle cell-hemoglobin C disease with crisis (disorder)
http://snomed.info/sct  417748003Sickle cell-hemoglobin D disease with crisis (disorder)
http://snomed.info/sct  440206000Hemoglobin SS disease with vasoocclusive crisis (disorder)
http://snomed.info/sct  444108000Acute sickle cell splenic sequestration crisis (disorder)
http://snomed.info/sct  783254003Hereditary persistence of fetal hemoglobin with sickle cell disease syndrome
http://snomed.info/sct  1153413001Acute sequestration of spleen due to sickle cell thalassemia with crisis (disorder)
http://snomed.info/sct  1153415008Acute splenic sequestration due to sickle cell hemoglobin C disease with crisis
http://snomed.info/sct  10759351000119103Sickle cell anaemia in mother complicating childbirth
http://snomed.info/sct  441482006History of sickle cell anaemia
http://hl7.org/fhir/sid/icd-10-cm  D57Sickle-cell disorders
http://hl7.org/fhir/sid/icd-10-cm  D57.0Hb-SS disease with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.00Hb-SS disease with crisis, unspecified
http://hl7.org/fhir/sid/icd-10-cm  D57.01Hb-SS disease with acute chest syndrome
http://hl7.org/fhir/sid/icd-10-cm  D57.02Hb-SS disease with splenic sequestration
http://hl7.org/fhir/sid/icd-10-cm  D57.03Hb-SS disease with cerebral vascular involvement
http://hl7.org/fhir/sid/icd-10-cm  D57.04Hb-SS disease with dactylitis
http://hl7.org/fhir/sid/icd-10-cm  D57.09Hb-SS disease with crisis with other specified complication
http://hl7.org/fhir/sid/icd-10-cm  D57.2Sickle-cell/Hb-C disease
http://hl7.org/fhir/sid/icd-10-cm  D57.20Sickle-cell/Hb-C disease without crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.21Sickle-cell/Hb-C disease with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.211Sickle-cell/Hb-C disease with acute chest syndrome
http://hl7.org/fhir/sid/icd-10-cm  D57.212Sickle-cell/Hb-C disease with splenic sequestration
http://hl7.org/fhir/sid/icd-10-cm  D57.213Sickle-cell/Hb-C disease with cerebral vascular involvement
http://hl7.org/fhir/sid/icd-10-cm  D57.214Sickle-cell/Hb-C disease with dactylitis
http://hl7.org/fhir/sid/icd-10-cm  D57.218Sickle-cell/Hb-C disease with crisis with other specified complication
http://hl7.org/fhir/sid/icd-10-cm  D57.219Sickle-cell/Hb-C disease with crisis, unspecified
http://hl7.org/fhir/sid/icd-10-cm  D57.3Sickle-cell trait
http://hl7.org/fhir/sid/icd-10-cm  D57.4Sickle-cell thalassemia
http://hl7.org/fhir/sid/icd-10-cm  D57.40Sickle-cell thalassemia without crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.41Sickle-cell thalassemia, unspecified, with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.411Sickle-cell thalassemia, unspecified, with acute chest syndrome
http://hl7.org/fhir/sid/icd-10-cm  D57.412Sickle-cell thalassemia, unspecified, with splenic sequestration
http://hl7.org/fhir/sid/icd-10-cm  D57.413Sickle-cell thalassemia, unspecified, with cerebral vascular involvement
http://hl7.org/fhir/sid/icd-10-cm  D57.414Sickle-cell thalassemia, unspecified, with dactylitis
http://hl7.org/fhir/sid/icd-10-cm  D57.418Sickle-cell thalassemia, unspecified, with crisis with other specified complication
http://hl7.org/fhir/sid/icd-10-cm  D57.419Sickle-cell thalassemia, unspecified, with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.42Sickle-cell thalassemia beta zero without crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.43Sickle-cell thalassemia beta zero with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.431Sickle-cell thalassemia beta zero with acute chest syndrome
http://hl7.org/fhir/sid/icd-10-cm  D57.432Sickle-cell thalassemia beta zero with splenic sequestration
http://hl7.org/fhir/sid/icd-10-cm  D57.433Sickle-cell thalassemia beta zero with cerebral vascular involvement
http://hl7.org/fhir/sid/icd-10-cm  D57.434Sickle-cell thalassemia beta zero with dactylitis
http://hl7.org/fhir/sid/icd-10-cm  D57.438Sickle-cell thalassemia beta zero with crisis with other specified complication
http://hl7.org/fhir/sid/icd-10-cm  D57.439Sickle-cell thalassemia beta zero with crisis, unspecified
http://hl7.org/fhir/sid/icd-10-cm  D57.44Sickle-cell thalassemia beta plus without crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.45Sickle-cell thalassemia beta plus with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.451Sickle-cell thalassemia beta plus with acute chest syndrome
http://hl7.org/fhir/sid/icd-10-cm  D57.452Sickle-cell thalassemia beta plus with splenic sequestration
http://hl7.org/fhir/sid/icd-10-cm  D57.453Sickle-cell thalassemia beta plus with cerebral vascular involvement
http://hl7.org/fhir/sid/icd-10-cm  D57.454Sickle-cell thalassemia beta plus with dactylitis
http://hl7.org/fhir/sid/icd-10-cm  D57.458Sickle-cell thalassemia beta plus with crisis with other specified complication
http://hl7.org/fhir/sid/icd-10-cm  D57.459Sickle-cell thalassemia beta plus with crisis, unspecified
http://hl7.org/fhir/sid/icd-10-cm  D57.8Other sickle-cell disorders
http://hl7.org/fhir/sid/icd-10-cm  D57.80Other sickle-cell disorders without crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.81Other sickle-cell disorders with crisis
http://hl7.org/fhir/sid/icd-10-cm  D57.811Other sickle-cell disorders with acute chest syndrome
http://hl7.org/fhir/sid/icd-10-cm  D57.812Other sickle-cell disorders with splenic sequestration
http://hl7.org/fhir/sid/icd-10-cm  D57.813Other sickle-cell disorders with cerebral vascular involvement
http://hl7.org/fhir/sid/icd-10-cm  D57.814Other sickle-cell disorders with dactylitis
http://hl7.org/fhir/sid/icd-10-cm  D57.818Other sickle-cell disorders with crisis with other specified complication
http://hl7.org/fhir/sid/icd-10-cm  D57.819Other sickle-cell disorders with crisis, unspecified

Explanation of the columns that may appear on this page:

Level A few code lists that FHIR defines are hierarchical - each code is assigned a level. In this scheme, some codes are under other codes, and imply that the code they are under also applies
System The source of the definition of the code (when the value set draws in codes defined elsewhere)
Code The code (used as the code in the resource instance)
Display The display (used in the display element of a Coding). If there is no display, implementers should not simply display the code, but map the concept into their application
Definition An explanation of the meaning of the concept
Comments Additional notes about how to use the code