2022 CDC Clinical Practice Guideline for Prescribing Opioids Implementation Guide
2022.1.0 - CI Build

2022 CDC Clinical Practice Guideline for Prescribing Opioids Implementation Guide, published by Centers for Disease Control and Prevention (CDC). This guide is not an authorized publication; it is the continuous build for version 2022.1.0 built by the FHIR (HL7® FHIR® Standard) CI Build. This version is based on the current content of https://github.com/cqframework/opioid-cds-r4/ and changes regularly. See the Directory of published versions

: Sickle-cell diseases - XML Representation

Active as of 2023-05-25

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<ValueSet xmlns="http://hl7.org/fhir">
  <id value="sickle-cell-diseases"/>
  <meta>
    <profile
             value="http://fhir.org/guides/cdc/opioid-cds/StructureDefinition/cdc-valueset"/>
    <profile
             value="http://hl7.org/fhir/uv/cpg/StructureDefinition/cpg-computablevalueset"/>
    <profile
             value="http://hl7.org/fhir/uv/cpg/StructureDefinition/cpg-executablevalueset"/>
  </meta>
  <text>
    <status value="generated"/>
    <div xmlns="http://www.w3.org/1999/xhtml"><div style="border: black 1px dotted; background-color: #EEEEEE; padding: 8px; margin-bottom: 8px"><p>Expansion based on: </p><ul><li>system http://hl7.org/fhir/sid/icd-10-cm version 2021</li><li>SNOMED CT United States edition 01-Mar 2023</li></ul></div><p>This value set expansion contains 75 concepts.</p><table class="codes"><tr><td style="white-space:nowrap"><b>Code</b></td><td><b>System</b></td><td><b>Display</b></td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-417357006"> </a>  <a href="http://snomed.info/id/417357006">417357006</a></td><td>http://snomed.info/sct</td><td>Sickling disorder due to hemoglobin S (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-23269001"> </a>  <a href="http://snomed.info/id/23269001">23269001</a></td><td>http://snomed.info/sct</td><td>Double heterozygous sickling disorder (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-25472008"> </a>  <a href="http://snomed.info/id/25472008">25472008</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin D disease (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-35434009"> </a>  <a href="http://snomed.info/id/35434009">35434009</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin C disease (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-36472007"> </a>  <a href="http://snomed.info/id/36472007">36472007</a></td><td>http://snomed.info/sct</td><td>Sickle cell-thalassemia disease (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-47024008"> </a>  <a href="http://snomed.info/id/47024008">47024008</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin E disease (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-127040003"> </a>  <a href="http://snomed.info/id/127040003">127040003</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin SS disease (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-127041004"> </a>  <a href="http://snomed.info/id/127041004">127041004</a></td><td>http://snomed.info/sct</td><td>Sickle cell-beta-thalassemia (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-127042006"> </a>  <a href="http://snomed.info/id/127042006">127042006</a></td><td>http://snomed.info/sct</td><td>Sickle cell beta plus thalassemia (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-127043001"> </a>  <a href="http://snomed.info/id/127043001">127043001</a></td><td>http://snomed.info/sct</td><td>Sickle cell-beta^0^-thalassemia (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-127044007"> </a>  <a href="http://snomed.info/id/127044007">127044007</a></td><td>http://snomed.info/sct</td><td>Sickle cell-delta beta^0^-thalassemia (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-127045008"> </a>  <a href="http://snomed.info/id/127045008">127045008</a></td><td>http://snomed.info/sct</td><td>Sickle cell anemia with coexistent alpha-thalassemia (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-127047000"> </a>  <a href="http://snomed.info/id/127047000">127047000</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin Lepore disease (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-127048005"> </a>  <a href="http://snomed.info/id/127048005">127048005</a></td><td>http://snomed.info/sct</td><td>Sickle cell-Hemoglobin O Arab disease (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-234391009"> </a>  <a href="http://snomed.info/id/234391009">234391009</a></td><td>http://snomed.info/sct</td><td>Sickle cell anemia with high hemoglobin F (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-416484003"> </a>  <a href="http://snomed.info/id/416484003">416484003</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin E disease with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-416826005"> </a>  <a href="http://snomed.info/id/416826005">416826005</a></td><td>http://snomed.info/sct</td><td>Sickle cell-thalassemia disease with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-417048006"> </a>  <a href="http://snomed.info/id/417048006">417048006</a></td><td>http://snomed.info/sct</td><td>Sickle cell-thalassemia disease without crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-417279003"> </a>  <a href="http://snomed.info/id/417279003">417279003</a></td><td>http://snomed.info/sct</td><td>Hemoglobin S sickling disorder with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-417425009"> </a>  <a href="http://snomed.info/id/417425009">417425009</a></td><td>http://snomed.info/sct</td><td>Hemoglobin SS disease with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-417517009"> </a>  <a href="http://snomed.info/id/417517009">417517009</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin C disease with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-417748003"> </a>  <a href="http://snomed.info/id/417748003">417748003</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin D disease with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-440206000"> </a>  <a href="http://snomed.info/id/440206000">440206000</a></td><td>http://snomed.info/sct</td><td>Hemoglobin SS disease with vasoocclusive crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-444108000"> </a>  <a href="http://snomed.info/id/444108000">444108000</a></td><td>http://snomed.info/sct</td><td>Acute sickle cell splenic sequestration crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-783254003"> </a>  <a href="http://snomed.info/id/783254003">783254003</a></td><td>http://snomed.info/sct</td><td>Hereditary persistence of fetal hemoglobin with sickle cell disease syndrome (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-1153413001"> </a>  <a href="http://snomed.info/id/1153413001">1153413001</a></td><td>http://snomed.info/sct</td><td>Acute sequestration of spleen due to sickle cell thalassemia with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-1153415008"> </a>  <a href="http://snomed.info/id/1153415008">1153415008</a></td><td>http://snomed.info/sct</td><td>Acute sequestration of spleen due to sickle cell hemoglobin C disease with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-10759351000119103"> </a>  <a href="http://snomed.info/id/10759351000119103">10759351000119103</a></td><td>http://snomed.info/sct</td><td>Sickle cell anemia in mother complicating childbirth (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="http---snomed.info-sct-441482006"> </a>  <a href="http://snomed.info/id/441482006">441482006</a></td><td>http://snomed.info/sct</td><td>History of sickle cell anemia (situation)</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57"> </a>  D57</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell disorders</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.0"> </a>  D57.0</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with crisis</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.00"> </a>  D57.00</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with crisis, unspecified</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.01"> </a>  D57.01</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with acute chest syndrome</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.02"> </a>  D57.02</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with splenic sequestration</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.03"> </a>  D57.03</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with cerebral vascular involvement</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.09"> </a>  D57.09</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with crisis with other specified complication</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.2"> </a>  D57.2</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.20"> </a>  D57.20</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease without crisis</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.21"> </a>  D57.21</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with crisis</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.211"> </a>  D57.211</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with acute chest syndrome</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.212"> </a>  D57.212</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with splenic sequestration</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.213"> </a>  D57.213</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with cerebral vascular involvement</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.218"> </a>  D57.218</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with crisis with other specified complication</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.219"> </a>  D57.219</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with crisis, unspecified</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.3"> </a>  D57.3</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell trait</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.4"> </a>  D57.4</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.40"> </a>  D57.40</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia without crisis</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.41"> </a>  D57.41</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with crisis</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.411"> </a>  D57.411</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with acute chest syndrome</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.412"> </a>  D57.412</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with splenic sequestration</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.413"> </a>  D57.413</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with cerebral vascular involvement</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.418"> </a>  D57.418</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with crisis with other specified complication</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.419"> </a>  D57.419</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with crisis</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.42"> </a>  D57.42</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero without crisis</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.43"> </a>  D57.43</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with crisis</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.431"> </a>  D57.431</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with acute chest syndrome</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.432"> </a>  D57.432</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with splenic sequestration</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.433"> </a>  D57.433</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with cerebral vascular involvement</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.438"> </a>  D57.438</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with crisis with other specified complication</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.439"> </a>  D57.439</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with crisis, unspecified</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.44"> </a>  D57.44</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus without crisis</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.45"> </a>  D57.45</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with crisis</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.451"> </a>  D57.451</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with acute chest syndrome</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.452"> </a>  D57.452</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with splenic sequestration</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.453"> </a>  D57.453</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with cerebral vascular involvement</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.458"> </a>  D57.458</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with crisis with other specified complication</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.459"> </a>  D57.459</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with crisis, unspecified</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.8"> </a>  D57.8</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.80"> </a>  D57.80</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders without crisis</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.81"> </a>  D57.81</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with crisis</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.811"> </a>  D57.811</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with acute chest syndrome</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.812"> </a>  D57.812</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with splenic sequestration</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.813"> </a>  D57.813</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with cerebral vascular involvement</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.818"> </a>  D57.818</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with crisis with other specified complication</td></tr><tr><td style="white-space:nowrap"><a name="http---hl7.org-fhir-sid-icd-10-cm-D57.819"> </a>  D57.819</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with crisis, unspecified</td></tr></table></div>
  </text>
  <extension
             url="http://fhir.org/guides/cdc/opioid-cds/StructureDefinition/cdc-valueset-clinical-focus">
    <valueString
                 value="Conditions due to Sickle-cell that can cause painful crisis to be used as exclusions for opioid use recommendations"/>
  </extension>
  <extension
             url="http://fhir.org/guides/cdc/opioid-cds/StructureDefinition/cdc-valueset-dataelement-scope">
    <valueString value="Condition"/>
  </extension>
  <extension
             url="http://fhir.org/guides/cdc/opioid-cds/StructureDefinition/cdc-valueset-inclusion-criteria">
    <valueString value="Coditions that cause red blood cell sickling"/>
  </extension>
  <extension
             url="http://fhir.org/guides/cdc/opioid-cds/StructureDefinition/cdc-valueset-exclusion-criteria">
    <valueString
                 value="Any sickle-cell disorder that does not result in painful crisis"/>
  </extension>
  <extension url="http://hl7.org/fhir/StructureDefinition/valueset-author">
    <valueContactDetail>
      <name value="MD Partners, Inc."/>
      <telecom>
        <system value="email"/>
        <value value="info@mdpartners.com"/>
      </telecom>
    </valueContactDetail>
  </extension>
  <extension
             url="http://hl7.org/fhir/uv/cpg/StructureDefinition/cpg-knowledgeCapability">
    <valueCode value="computable"/>
  </extension>
  <extension
             url="http://hl7.org/fhir/uv/cpg/StructureDefinition/cpg-knowledgeRepresentationLevel">
    <valueCode value="structured"/>
  </extension>
  <extension
             url="http://hl7.org/fhir/uv/cpg/StructureDefinition/cpg-knowledgeCapability">
    <valueCode value="executable"/>
  </extension>
  <extension
             url="http://hl7.org/fhir/uv/cpg/StructureDefinition/cpg-knowledgeRepresentationLevel">
    <valueCode value="executable"/>
  </extension>
  <extension
             url="http://hl7.org/fhir/uv/cpg/StructureDefinition/cpg-usageWarning">
    <valueString
                 value="This value set contains a point-in-time expansion enumerating the codes that meet the value set intent. As new versions of the code systems used by the value set are released, the contents of this expansion will need to be updated to incorporate newly defined codes that meet the value set intent. Before, and periodically during production use, the value set expansion contents SHOULD be updated. The value set expansion specifies the timestamp when the expansion was produced, SHOULD contain the parameters used for the expansion, and SHALL contain the codes that are obtained by evaluating the value set definition. If this is ONLY an executable value set, a distributable definition of the value set must be obtained to compute the updated expansion."/>
  </extension>
  <extension url="http://hl7.org/fhir/StructureDefinition/valueset-author">
    <valueContactDetail>
      <name value="MD Partners, Inc."/>
      <telecom>
        <system value="email"/>
        <value value="info@mdpartners.com"/>
      </telecom>
    </valueContactDetail>
  </extension>
  <url
       value="http://fhir.org/guides/cdc/opioid-cds/ValueSet/sickle-cell-diseases"/>
  <version value="2022.1.0"/>
  <name value="SICKLE_CELL_DISEASES"/>
  <title value="Sickle-cell diseases"/>
  <status value="active"/>
  <experimental value="false"/>
  <date value="2023-05-25T18:08:12-06:00"/>
  <publisher value="Centers for Disease Control and Prevention (CDC)"/>
  <contact>
    <telecom>
      <system value="url"/>
      <value value="https://www.cdc.gov"/>
    </telecom>
  </contact>
  <description value="Sickle-cell disorders that cause painful crisis"/>
  <jurisdiction>
    <coding>
      <system value="urn:iso:std:iso:3166"/>
      <code value="US"/>
    </coding>
  </jurisdiction>
  <purpose
           value="Conditions due to Sickle-cell that can cause painful crisis to be used as exclusions for opioid use recommendations"/>
  <copyright value="© CDC 2016+."/>
  <compose>
    <include>
      <system value="http://snomed.info/sct"/>
      <version value="http://snomed.info/sct/731000124108"/>
      <filter>
        <property value="concept"/>
        <op value="is-a"/>
        <value value="417357006"/>
      </filter>
    </include>
    <include>
      <system value="http://snomed.info/sct"/>
      <version value="http://snomed.info/sct/731000124108"/>
      <filter>
        <property value="concept"/>
        <op value="is-a"/>
        <value value="441482006"/>
      </filter>
    </include>
    <include>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <filter>
        <property value="concept"/>
        <op value="is-a"/>
        <value value="D57"/>
      </filter>
    </include>
    <exclude>
      <system value="http://snomed.info/sct"/>
      <version value="http://snomed.info/sct/731000124108"/>
      <filter>
        <property value="concept"/>
        <op value="is-a"/>
        <value value="416290001"/>
      </filter>
    </exclude>
    <exclude>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <filter>
        <property value="concept"/>
        <op value="is-a"/>
        <value value="D57.1"/>
      </filter>
    </exclude>
  </compose>
  <expansion>
    <extension
               url="http://hl7.org/fhir/StructureDefinition/valueset-unclosed">
      <valueBoolean value="true"/>
    </extension>
    <identifier value="urn:uuid:0281133f-6551-4663-a4e2-49b54cd41598"/>
    <timestamp value="2023-05-25T18:04:42.877Z"/>
    <parameter>
      <name value="version"/>
      <valueUri
                value="http://snomed.info/sct|http://snomed.info/sct/731000124108/version/20230301"/>
    </parameter>
    <parameter>
      <name value="version"/>
      <valueUri value="http://hl7.org/fhir/sid/icd-10-cm|2021"/>
    </parameter>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="417357006"/>
      <display value="Sickling disorder due to hemoglobin S (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="23269001"/>
      <display value="Double heterozygous sickling disorder (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="25472008"/>
      <display value="Sickle cell-hemoglobin D disease (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="35434009"/>
      <display value="Sickle cell-hemoglobin C disease (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="36472007"/>
      <display value="Sickle cell-thalassemia disease (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="47024008"/>
      <display value="Sickle cell-hemoglobin E disease (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127040003"/>
      <display value="Sickle cell-hemoglobin SS disease (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127041004"/>
      <display value="Sickle cell-beta-thalassemia (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127042006"/>
      <display value="Sickle cell beta plus thalassemia (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127043001"/>
      <display value="Sickle cell-beta^0^-thalassemia (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127044007"/>
      <display value="Sickle cell-delta beta^0^-thalassemia (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127045008"/>
      <display
               value="Sickle cell anemia with coexistent alpha-thalassemia (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127047000"/>
      <display value="Sickle cell-hemoglobin Lepore disease (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127048005"/>
      <display value="Sickle cell-Hemoglobin O Arab disease (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="234391009"/>
      <display value="Sickle cell anemia with high hemoglobin F (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="416484003"/>
      <display
               value="Sickle cell-hemoglobin E disease with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="416826005"/>
      <display
               value="Sickle cell-thalassemia disease with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="417048006"/>
      <display
               value="Sickle cell-thalassemia disease without crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="417279003"/>
      <display value="Hemoglobin S sickling disorder with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="417425009"/>
      <display value="Hemoglobin SS disease with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="417517009"/>
      <display
               value="Sickle cell-hemoglobin C disease with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="417748003"/>
      <display
               value="Sickle cell-hemoglobin D disease with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="440206000"/>
      <display
               value="Hemoglobin SS disease with vasoocclusive crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="444108000"/>
      <display
               value="Acute sickle cell splenic sequestration crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="783254003"/>
      <display
               value="Hereditary persistence of fetal hemoglobin with sickle cell disease syndrome (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="1153413001"/>
      <display
               value="Acute sequestration of spleen due to sickle cell thalassemia with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="1153415008"/>
      <display
               value="Acute sequestration of spleen due to sickle cell hemoglobin C disease with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="10759351000119103"/>
      <display
               value="Sickle cell anemia in mother complicating childbirth (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="441482006"/>
      <display value="History of sickle cell anemia (situation)"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57"/>
      <display value="Sickle-cell disorders"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.0"/>
      <display value="Hb-SS disease with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.00"/>
      <display value="Hb-SS disease with crisis, unspecified"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.01"/>
      <display value="Hb-SS disease with acute chest syndrome"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.02"/>
      <display value="Hb-SS disease with splenic sequestration"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.03"/>
      <display value="Hb-SS disease with cerebral vascular involvement"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.09"/>
      <display
               value="Hb-SS disease with crisis with other specified complication"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.2"/>
      <display value="Sickle-cell/Hb-C disease"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.20"/>
      <display value="Sickle-cell/Hb-C disease without crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.21"/>
      <display value="Sickle-cell/Hb-C disease with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.211"/>
      <display value="Sickle-cell/Hb-C disease with acute chest syndrome"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.212"/>
      <display value="Sickle-cell/Hb-C disease with splenic sequestration"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.213"/>
      <display
               value="Sickle-cell/Hb-C disease with cerebral vascular involvement"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.218"/>
      <display
               value="Sickle-cell/Hb-C disease with crisis with other specified complication"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.219"/>
      <display value="Sickle-cell/Hb-C disease with crisis, unspecified"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.3"/>
      <display value="Sickle-cell trait"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.4"/>
      <display value="Sickle-cell thalassemia"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.40"/>
      <display value="Sickle-cell thalassemia without crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.41"/>
      <display value="Sickle-cell thalassemia, unspecified, with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.411"/>
      <display
               value="Sickle-cell thalassemia, unspecified, with acute chest syndrome"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.412"/>
      <display
               value="Sickle-cell thalassemia, unspecified, with splenic sequestration"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.413"/>
      <display
               value="Sickle-cell thalassemia, unspecified, with cerebral vascular involvement"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.418"/>
      <display
               value="Sickle-cell thalassemia, unspecified, with crisis with other specified complication"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.419"/>
      <display value="Sickle-cell thalassemia, unspecified, with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.42"/>
      <display value="Sickle-cell thalassemia beta zero without crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.43"/>
      <display value="Sickle-cell thalassemia beta zero with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.431"/>
      <display
               value="Sickle-cell thalassemia beta zero with acute chest syndrome"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.432"/>
      <display
               value="Sickle-cell thalassemia beta zero with splenic sequestration"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.433"/>
      <display
               value="Sickle-cell thalassemia beta zero with cerebral vascular involvement"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.438"/>
      <display
               value="Sickle-cell thalassemia beta zero with crisis with other specified complication"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.439"/>
      <display
               value="Sickle-cell thalassemia beta zero with crisis, unspecified"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.44"/>
      <display value="Sickle-cell thalassemia beta plus without crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.45"/>
      <display value="Sickle-cell thalassemia beta plus with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.451"/>
      <display
               value="Sickle-cell thalassemia beta plus with acute chest syndrome"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.452"/>
      <display
               value="Sickle-cell thalassemia beta plus with splenic sequestration"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.453"/>
      <display
               value="Sickle-cell thalassemia beta plus with cerebral vascular involvement"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.458"/>
      <display
               value="Sickle-cell thalassemia beta plus with crisis with other specified complication"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.459"/>
      <display
               value="Sickle-cell thalassemia beta plus with crisis, unspecified"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.8"/>
      <display value="Other sickle-cell disorders"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.80"/>
      <display value="Other sickle-cell disorders without crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.81"/>
      <display value="Other sickle-cell disorders with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.811"/>
      <display value="Other sickle-cell disorders with acute chest syndrome"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.812"/>
      <display
               value="Other sickle-cell disorders with splenic sequestration"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.813"/>
      <display
               value="Other sickle-cell disorders with cerebral vascular involvement"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.818"/>
      <display
               value="Other sickle-cell disorders with crisis with other specified complication"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.819"/>
      <display value="Other sickle-cell disorders with crisis, unspecified"/>
    </contains>
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</ValueSet>